Primary Extraskeletal Ewing Sarcoma of the Thoracolumbar Epidural Space: Rare Case Report in a Child

Abstract Introduction Ewing sarcomas are a family of tumors that can be skeletal or extraskeletal origin. We report rare case child with sarcoma in the thoracolumbar epidural space. Case Report The patient was 1-year-old female sphincter alteration, flaccid paraplegia, and areflexia. A magnetic resonance imaging (MRI) scan showed large extensive lesion compression dural sac D6–L2 segment, left paravertebral extension through L1–L2 foramen. Laminotomy performed, subtotal resection lesion. histopathological immunohistochemical analyses indicated sarcoma. Due to child's age, radiotherapy not only chemotherapy, due aggressiveness neoplasm. rapid tumor recurrence ended up dying. Discussion Extraskeletal appear different locations body. They aggressive local distant metastases. In our case, combination MRI positron-emission tomography–computed tomography presented clearer result, especially presence metastasis. analysis, small blue cells clear cytoplasm indistinct nucleoli were observed. CD99 (MIC2) expression is highlighted. best treatment outcome would have been surgical chemotherapy radiotherapy. Conclusion reported which, despite surgery behaved very aggressively, leading an unfavorable prognosis.